Abstract
Posterior cortical atrophy (PCA) is a rare dementia, characterized by degeneration of the posterior parieto-occipital cortex, and degeneration of occipito-temporal and occipito-parietal streams of visual processing, which produced an early higher disorrder visuospatial and visual perceptual deficits often accompanied, or followed by features of Balint’s syndrome and Gerstmann’s Syndrome. The visual perceptual deficit is predominant in the clinical picture according to other cognitive symptoms like the compromise in memory and language. Three patients with this dementia are shown, which begun with symptoms of visual perceptual deficit and special disorientation without memory and language compromise. All the cases were verified with radiological findings, which demonstrate in all three, focal atrophy in the parieto-occipital cortex. Posterior cortical atrophy is a focal demential disorder characterized by visual perceptual deficit as initial manifestation, while other cognitive dominium such as memory, language and behavior are spare until advance stages of the disease. These cases were remarkably similar and concordant with the clinical description and neuroimaging characteristic of PCA report in the literature. It is relevant to recognize the PCA as a type of presenile dementia with clinical characteristic of its own which is separated and differentiated of the neuropsychogical profile of other dementias
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