Guillain-Barre Syndrome axonal variant in pediatrics: case report
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Keywords

acute inflammatory demyelinating polyradiculopathy
acute autoimmune neuropathy
acute infectious polyneuritis
Guillain-Barré Syndrome
pediatrics (MeSH)

Abstract

Guillain-Barre syndrome is an acute inflammatory polyradiculoneuropathy characterized by progressive symmetric weakness of distal onset associated with areflexia and mild sensory symptoms. The AMAN variant is a rare entity in Latin America. The case of a 6-year-old male patient, previously healthy, with a diagnosis of Guillain-Barre Syndrome, axonal variant, secondary to upper airway symptoms, is reported. The importance of the report lies in informing the pediatrician and other health professionals about the existence of this entity and thus increasing the diagnostic suspicion considering its low incidence. We also highlight the possibility of finding variability in the typical clinical forms of presentation, as was the case presented, since it is a subtype of the disease that is classically characterized as severe and with torpid evolution. It is also associated with frequent sequelae.

https://doi.org/10.22379/24224022358

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